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Code System Concept

Code System Concept Code	93557001
Code System Concept Name	Holorachischisis (disorder)
Code System Preferred Concept Name	Holorachischisis (disorder)
Concept Status	Published
Concept Status Date	03/01/2025
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	01/31/2002
SDO Date Created	01/31/2002
SDO Date Revised	01/31/2002
Description	Rachischisis is a neural tube defect, which occurs when the neural folds do not join at the midline and the undifferentiated neuroectoderm remains exposed. Rachischisis totalis (holorachischisis) is the extreme form in which the entire spinal cord remains open.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
154876010	Holorachischisis	Active	Synonym	false	false
4279482017	Rachischisis totalis	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1
Disease	10 , 9 , 8 , 7 , 6 , 5 , 4 , 3 , 2 , 1
Meningomyelocele/Spina Bifida - Newborn (NCHS)	2 , 1
Problem Value Set	3 , 2

Parent Concepts No parent concepts present.	Other Relationships No other relationships present.
Child Concepts No child concepts present.