Code System Concept

Code System Concept

Code System Concept Code	829971006
Code System Concept Name	Non-amyloid monoclonal immunoglobulin deposition disease (disorder)
Code System Preferred Concept Name	Non-amyloid monoclonal immunoglobulin deposition disease (disorder)
Concept Status	Published
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	07/31/2020
SDO Date Created	07/31/2020
SDO Date Revised	07/31/2020
Description	A rare secondary glomerular disease characterised by proteinuria, dysproteinaemia, nephrotic syndrome, and nodular glomerulopathy leading to renal failure, with or without extra-renal manifestations. The renal biopsy shows typical deposits of monoclonal immunoglobulins that do not show a fibrillar organisation and are negative for Congo red staining. Associated signs and symptoms depend on the involvement of other organs, liver, heart, nerve fibres, gastrointestinal tract or skin.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
3880131011	Non-amyloid monoclonal immunoglobulin deposition disease	Active	Synonym	false	false
3880132016	Randall disease	Active	Synonym	false	false
3880133014	Non-amyloid MIDD (monoclonal immunoglobulin deposition disease)	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1
Disease	10

Parent Concepts

Parent Concepts

Parent/Child (Relationship Type)

Other Relationships

No other relationships present.

Child Concepts

Non-amyloid monoclonal immunoglobulin deposition disease (disorder) {829971006 , SNOMED-CT }

Parent/Child (Relationship Type)

Heavy chain deposition disease (disorder) {148041000146104 , SNOMED-CT }