Code System Concept

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Code System Concept

Code System Concept Code	780841002
Code System Concept Name	Classic mast cell leukemia (disorder)
Code System Preferred Concept Name	Classic mast cell leukemia (disorder)
Concept Status	Retired
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept	Concept Code: 110002002 Concept Name: Mast cell leukemia (disorder) Code System: SNOMED-CT
SDO Concept Status	Inactive
SDO Concept Status Date	07/31/2020
SDO Date Created	01/31/2019
SDO Date Revised	07/31/2020
Description	A very rare aggressive form of systemic mastocytosis characterized by abnormal growth and proliferation of neoplastic mast cells (>20%) in the bone marrow and/or blood, as well as other tissues such as the liver, peritoneum, spleen or bones. Patients typically present with symptoms related to mast cell activation (for example hot flushes, fever, malaise, diarrhea, tachycardia), weight loss, anorexia and hepatosplenomegaly or less frequently cutaneous mastocytosis. Gastroduodenal ulcers (often complicated by hemorrhage), ascites and portal hypertension have also been reported.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
3743927017	Classic mast cell leukemia	Active	Synonym	false	false
3743928010	Classic mast cell leukaemia	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Disease	9 , 8
Problem Value Set	3

Parent Concepts Parent Concepts Parent/Child (Relationship Type) Leukemia, disease (disorder) {93143009 , SNOMED-CT } Malignant white blood cell disorder (disorder) {277543005 , SNOMED-CT } Mast cell leukemia (disorder) {110002002 , SNOMED-CT } Mast cell neoplasm (disorder) {414653009 , SNOMED-CT } Systemic mast cell disease (disorder) {397016004 , SNOMED-CT }	Other Relationships No other relationships present.
Child Concepts No child concepts present.

Page last reviewed:June 20, 2024
Page last updated:June 20, 2024
Content source:
- Centers for Disease Control and Prevention,