Application Version: 4.0.6.10
Content Version: 2024.07.12
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Code System Concept
Code System Concept Code | 770402000 |
Code System Concept Name | Aleukemic mast cell leukemia (disorder) |
Code System Preferred Concept Name | Aleukemic mast cell leukemia (disorder) |
Concept Status | Published |
Concept Status Date | 09/01/2024 |
Code System Name | SNOMED-CT |
Concept Details
Code System Code | PH_SNOMED-CT |
Code System OID | 2.16.840.1.113883.6.96 |
HL7 Table 0396 Code | SCT |
Superseded By Concept | |
SDO Concept Status | Inactive |
SDO Concept Status Date | 01/31/2019 |
SDO Date Created | 01/31/2019 |
SDO Date Revised | 03/31/2023 |
Description | A very rare aggressive form of systemic mastocytosis characterized by abnormal growth and proliferation of neoplastic mast cells in the bone marrow and/or blood, as well as other tissues such as the liver, peritoneum, spleen or bones. Patients typically present with symptoms related to mast cell activation (for example hot flushes, fever, malaise, diarrhea, tachycardia), weight loss, anorexia, hepatosplenomegaly or less frequently cutaneous mastocytosis. Gastroduodenal ulcers (often complicated by hemorrhage), ascites and portal hypertension have also been reported. |
Sequence |
Extended Properties
No extended properties.
Concept Alternate Designations
SDO Designation ID | Concept Designation Description | Status | Designation Type | PHIN Preferred Term Flag | Code Flag |
---|---|---|---|---|---|
3700697011 | Aleukemic mast cell leukemia | Active | Synonym | false | false |
3700699014 | Aleukaemic mast cell leukaemia | Active | Synonym | false | false |
Parent Concepts
Parent Concepts
Parent/Child (Relationship Type)
Aleukemic leukemia (disorder)
{302856006
, SNOMED-CT
}
Leukemia, disease (disorder)
{93143009
, SNOMED-CT
}
Malignant white blood cell disorder (disorder)
{277543005
, SNOMED-CT
}
Mast cell leukemia (disorder)
{110002002
, SNOMED-CT
}
Mast cell neoplasm (disorder)
{414653009
, SNOMED-CT
}
Systemic mast cell disease (disorder)
{397016004
, SNOMED-CT
}
|
Other Relationships
No other relationships present.
|
Child Concepts
No child concepts present.
|
- Page last reviewed:June 20, 2024
- Page last updated:June 20, 2024
- Content source: