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Code System Concept

Code System Concept Code	734023003
Code System Concept Name	Sporadic adult-onset ataxia of unknown etiology (disorder)
Code System Preferred Concept Name	Sporadic adult-onset ataxia of unknown etiology (disorder)
Concept Status	Published
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	07/31/2017
SDO Date Created	07/31/2017
SDO Date Revised	07/31/2017
Description	Non-hereditary degenerative ataxia with characteristics of slowly progressive cerebellar syndrome (with ataxia of stance and gait, upper limb dysmetria and intention tremor, ataxic speech, and oculomotor abnormalities), presenting in adulthood (at around 50 years of age), that is not due to a known cause. Extracerebellar symptoms (e.g., decreased vibration sense and absent or decreased ankle reflexes), polyneuropathy and mild autonomic dysfunction may also be present. Mild cognitive impairment has also rarely been reported.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
3481957010	Sporadic adult-onset ataxia of unknown etiology	Active	Synonym	false	false
3481958017	Sporadic adult-onset ataxia of unknown aetiology	Active	Synonym	false	false
3481959013	Idiopathic late-onset cerebellar ataxia	Active	Synonym	false	false
3481960015	Sporadic adult-onset ataxia of unknown origin	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1
Disease	10 , 9 , 8 , 7
Problem Value Set	3

Parent Concepts Parent Concepts Parent/Child (Relationship Type) Ataxia (finding) {20262006 , SNOMED-CT } Cerebellar ataxia (disorder) {85102008 , SNOMED-CT } Cerebellar degeneration (disorder) {95646004 , SNOMED-CT } Degenerative disorder (disorder) {362975008 , SNOMED-CT } Idiopathic disease (disorder) {41969006 , SNOMED-CT } Late onset cerebellar ataxia (disorder) {230232005 , SNOMED-CT }	Other Relationships No other relationships present.
Child Concepts No child concepts present.