Code System Concept

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Code System Concept

Code System Concept Code	1336114003
Code System Concept Name	Pyogenic arthritis, pyoderma gangrenosum, acne, hidradenitis suppurativa syndrome (disorder)
Code System Preferred Concept Name	Pyogenic arthritis, pyoderma gangrenosum, acne, hidradenitis suppurativa syndrome (disorder)
Concept Status	Published
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	09/01/2024
SDO Date Created	06/01/2024
SDO Date Revised	06/01/2024
Description	A rare autoinflammatory syndrome with characteristics of a chronic-relapsing course of the combination of pyogenic arthritis, pyoderma gangrenosum, acne, and hidradenitis suppurativa (which, in addition to axillae and inguinal folds, can be observed on the face, neck, scalp, back, and buttocks, among others). Typical age of onset is adolescence to young adulthood, with the different signs and symptoms appearing simultaneously or subsequently.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
5363452014	PAPASH syndrome	Active	Synonym	false	false
5363453016	PAPASH (pyogenic arthritis, pyoderma gangrenosum, acne, hidradenitis suppurativa) syndrome	Active	Synonym	false	false
5363455011	Pyogenic arthritis, pyoderma gangrenosum, acne, hidradenitis suppurativa syndrome	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1

Parent Concepts

Parent Concepts

Parent/Child (Relationship Type)

Acne (disorder) {11381005 , SNOMED-CT } Autoinflammatory disease (disorder) {42111000175103 , SNOMED-CT } Chronic arthropathy (disorder) {38850007 , SNOMED-CT } Chronic dermatitis (disorder) {34936007 , SNOMED-CT } Chronic disease of immune function (disorder) {413834006 , SNOMED-CT } Chronic disease of immune structure (disorder) {413835007 , SNOMED-CT } Chronic infectious disease (disorder) {177010002 , SNOMED-CT } Genetic disease (disorder) {782964007 , SNOMED-CT } Hidradenitis suppurativa pyoderma gangrenosum complex (disorder) {1254916008 , SNOMED-CT } Suppurative arthritis (disorder) {372939007 , SNOMED-CT }

Other Relationships

No other relationships present.

Child Concepts

No child concepts present.

Page last reviewed:June 20, 2024
Page last updated:June 20, 2024
Content source:
- Centers for Disease Control and Prevention,