Code System Concept

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Code System Concept

Code System Concept Code	1303909005
Code System Concept Name	Congenital spinal dermal sinus (disorder)
Code System Preferred Concept Name	Congenital spinal dermal sinus (disorder)
Concept Status	Published
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	09/01/2024
SDO Date Created	03/01/2024
SDO Date Revised	03/01/2024
Description	A rare closed dysraphism with stalk characterized by a dorsal midline dermal sinus tract lined by keratinizing stratified squamous epithelium extending to the intrathecal space. Other components such as hair follicles and shafts, mesenchymal derivatives (blood vessels and fibrous tissue) and occasionally nerve fibers can be observed. Inflamed granulation tissue containing mixed neutrophils, plasma cells, lymphocytes, and histiocytes is consistently found in the tract. It can also be associated with an intradural dermoid cyst. This malformation is at risk to cause intrathecal infections (meningitis, empyema) that justify prophylactic surgery.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
5308386014	Dermal sinus tract	Active	Synonym	false	false
5308391010	Congenital spinal dermal sinus	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1

Parent Concepts

Parent Concepts

Parent/Child (Relationship Type)

Congenital anomaly of back (disorder) {363025000 , SNOMED-CT } Congenital anomaly of thorax (disorder) {363035006 , SNOMED-CT } Congenital anomaly of upper trunk (disorder) {363037003 , SNOMED-CT } Congenital dermal sinus (disorder) {70499005 , SNOMED-CT } Disorder of soft tissue of trunk (disorder) {280133005 , SNOMED-CT } Fistula (disorder) {428794004 , SNOMED-CT } Neural tube defect (disorder) {253098009 , SNOMED-CT } Structural developmental anomalies of neurenteric canal (disorder) {249491000119100 , SNOMED-CT }

Other Relationships

No other relationships present.

Child Concepts

No child concepts present.

Page last reviewed:June 20, 2024
Page last updated:June 20, 2024
Content source:
- Centers for Disease Control and Prevention,