Code System Concept

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Code System Concept

Code System Concept Code	1255207005
Code System Concept Name	Immunoglobulin G4 related eosinophilic angiocentric fibrosis (disorder)
Code System Preferred Concept Name	Immunoglobulin G4 related eosinophilic angiocentric fibrosis (disorder)
Concept Status	Published
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	03/01/2023
SDO Date Created	10/31/2022
SDO Date Revised	10/31/2022
Description	A rare otorhinolaryngologic disease with characteristics of an indolent submucosal mass of variable size and extent, most commonly arising in the anterior nasal cavity, involving the nasal septum and lateral nasal wall and potentially extending into the adjacent sinuses. Occurrence in the larynx and lower respiratory tract or the orbit is rare. Histological examination shows concentric angiocentric stromal fibrosis (onionskin fibrosis) and prominent eosinophils. Increased numbers of IgG4-positive plasma cells in the lesion may also be observed, in addition to elevated serum IgG4. Patients typically present with long-standing obstructive symptoms.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
5145299011	IgG4-related eosinophilic angiocentric fibrosis	Active	Synonym	false	false
5145300015	Eosinophilic angiocentric fibrosis	Active	Synonym	false	false
5145301016	Immunoglobulin G4 related eosinophilic angiocentric fibrosis	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1

Parent Concepts Parent Concepts Parent/Child (Relationship Type) Disorder characterized by eosinophilia (disorder) {419455006 , SNOMED-CT } Ear, nose and throat disorder (disorder) {232208008 , SNOMED-CT } Immunoglobulin G4 related disease (disorder) {10743271000119103 , SNOMED-CT }	Other Relationships No other relationships present.
Child Concepts No child concepts present.

Page last reviewed:June 20, 2024
Page last updated:June 20, 2024
Content source:
- Centers for Disease Control and Prevention,