Code System Concept

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Code System Concept

Code System Concept Code	1231180000
Code System Concept Name	Papillary intralymphatic angioendothelioma (disorder)
Code System Preferred Concept Name	Papillary intralymphatic angioendothelioma (disorder)
Concept Status	Published
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	09/01/2022
SDO Date Created	06/30/2022
SDO Date Revised	06/30/2022
Description	A rare vascular tumour characterised by an ill-defined, slowly growing, asymptomatic cutaneous plaque or nodule mostly involving the limbs, in fewer cases the trunk. The tumour is composed of lymphatic-like channels with prominent intraluminal papillary tufts with hyaline cores lined by hobnail endothelial cells. It is locally aggressive, while metastasis is rare. Infants and children are much more often affected than adults.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
5071782014	Endovascular papillary angioendothelioma	Active	Synonym	false	false
5071784010	Dabska tumor	Active	Synonym	false	false
5071785011	Primary intralymphatic angioendothelioma	Active	Synonym	false	false
5071786012	Dabska tumour	Active	Synonym	false	false
5072171013	Papillary intralymphatic angioendothelioma	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1

Parent Concepts Parent Concepts Parent/Child (Relationship Type) Neoplasm of uncertain behavior of skin (disorder) {95087004 , SNOMED-CT } Vascular neoplasm of skin (disorder) {400132000 , SNOMED-CT }	Other Relationships No other relationships present.
Child Concepts Papillary intralymphatic angioendothelioma (disorder) {1231180000 , SNOMED-CT } Parent/Child (Relationship Type) Papillary intralymphatic angioendothelioma of childhood (disorder) {254799002 , SNOMED-CT }

Page last reviewed:June 20, 2024
Page last updated:June 20, 2024
Content source:
- Centers for Disease Control and Prevention,