Code System Concept

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Code System Concept

Code System Concept Code	1231148002
Code System Concept Name	Linear verrucous nevus syndrome (disorder)
Code System Preferred Concept Name	Linear verrucous nevus syndrome (disorder)
Concept Status	Published
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	09/01/2022
SDO Date Created	06/30/2022
SDO Date Revised	06/30/2022
Description	A rare skin disease with characteristics of a hamartomatous epidermal lesion presenting as a linear array of verrucous, hyperkeratotic papules that often coalesce into plaques and are formed along the lines of Blaschko. The condition is associated with involvement of other organ systems, mainly brain, eye and skeletal system. It is the result of mosaic post-zygotic mutations and most commonly presents at birth but may occur anytime during childhood rarely also in adulthood.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
5071667011	Linear verrucous naevus syndrome	Active	Synonym	false	false
5071668018	Linear verrucous nevus syndrome	Active	Synonym	false	false
5071669014	Linear hamartoma syndrome	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1

Parent Concepts Parent Concepts Parent/Child (Relationship Type) Systematized epidermal nevus (disorder) {239108002 , SNOMED-CT }	Other Relationships No other relationships present.
Child Concepts No child concepts present.

Page last reviewed:June 20, 2024
Page last updated:June 20, 2024
Content source:
- Centers for Disease Control and Prevention,