Code System Concept

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Code System Concept

Code System Concept Code	1187464007
Code System Concept Name	Clear cell sarcoma of kidney (disorder)
Code System Preferred Concept Name	Clear cell sarcoma of kidney (disorder)
Concept Status	Published
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	09/01/2022
SDO Date Created	01/31/2022
SDO Date Revised	01/31/2022
Description	A rare primary genetic renal tumour usually characterised by a unilateral, unicentric, morphologically diverse tumour that arises from the renal medulla and has a tendency for vascular invasion. Clinically it presents with a palpable abdominal mass, abdominal or flank pain, haematuria, anaemia and/or fatigue. Metastatic spread to lymph nodes, bones, lungs, retroperitoneum, brain and liver is common at time of diagnosis and therefore bone pain, cough or neurological compromise may be associated. Metastasis to unusual sites, such as the scalp, neck, nasopharynx, axilla, orbits and epidural space have been reported.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
4673873017	Clear cell sarcoma of kidney	Active	Synonym	false	false
4673875012	CCSK - clear cell sarcoma of kidney	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1

Parent Concepts Parent Concepts Parent/Child (Relationship Type) Genetic disease (disorder) {782964007 , SNOMED-CT } Primary malignant neoplasm of kidney (disorder) {93849006 , SNOMED-CT } Sarcoma of kidney (disorder) {254918001 , SNOMED-CT }	Other Relationships No other relationships present.
Child Concepts Clear cell sarcoma of kidney (disorder) {1187464007 , SNOMED-CT } Parent/Child (Relationship Type) Primary clear cell sarcoma of kidney (disorder) {1268543003 , SNOMED-CT }

Page last reviewed:June 20, 2024
Page last updated:June 20, 2024
Content source:
- Centers for Disease Control and Prevention,