Code System Concept

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Code System Concept

Code System Concept Code	1187124004
Code System Concept Name	Apolipoprotein A-IV amyloidosis (disorder)
Code System Preferred Concept Name	Apolipoprotein A-IV amyloidosis (disorder)
Concept Status	Published
Concept Status Date	09/01/2024
Code System Name	SNOMED-CT

Concept Relationships
Concept Details

Concept Details

Code System Code	PH_SNOMED-CT
Code System OID	2.16.840.1.113883.6.96
HL7 Table 0396 Code	SCT
Superseded By Concept
SDO Concept Status	Active
SDO Concept Status Date	09/01/2022
SDO Date Created	11/30/2021
SDO Date Revised	11/30/2021
Description	A rare systemic amyloidosis with characteristics of slowly progressive renal dysfunction, increased serum creatinine, mostly normal urine analysis with no significant proteinuria and associated heart disease. Cardiac involvement presents as hypertrophic obstructive cardiomyopathy, left ventricular outflow tract obstruction, coronary artery disease and conduction system abnormalities. Histology reveals renal tubular atrophy, interstitial fibrosis, glomerular sclerosis and medullar amyloid deposits.
Sequence

Extended Properties

No extended properties.

Concept Alternate Designations

SDO Designation ID	Concept Designation Description	Status	Designation Type	PHIN Preferred Term Flag	Code Flag
4670002012	AApoAIV (apolipoprotein A-IV) amyloidosis	Active	Synonym	false	false
4670003019	Apolipoprotein A-IV amyloidosis	Active	Synonym	false	false

Associated Value Sets

Value Set Name	Version(s)
Clinical Finding (NNDSS)	2 , 1

Parent Concepts Parent Concepts Parent/Child (Relationship Type) Amyloid nephropathy (disorder) {48713002 , SNOMED-CT } Renal disorders in systemic disease (disorder) {236498004 , SNOMED-CT } Systemic amyloidosis (disorder) {89449005 , SNOMED-CT } Toxic nephropathy (disorder) {236514003 , SNOMED-CT }	Other Relationships No other relationships present.
Child Concepts No child concepts present.

Page last reviewed:June 20, 2024
Page last updated:June 20, 2024
Content source:
- Centers for Disease Control and Prevention,